The Rabbit Anti-PAH/Phenylalanine Hydroxylase Antibody from MyBioSource.com is a Rabbit Polyclonal antibody to PAH, and Phenylalanine Hydroxylase. This antibody recognizes Human, Mouse, and Rat antigen. The Rabbit Anti-PAH/Phenylalanine Hydroxylase Antibody has been validated for the following applications: Immunohistochemistry, and Western Blot.
Description
Phenylalanine hydroxylase (PAH) is an enzyme that catalyzes the hydroxylation of the aromatic side-chain of phenylalanine to generate tyrosine. It is one of three members of the biopterin-dependent aromatic amino acid hydroxylases, a class of monooxygenase that uses tetrahydrobiopterin (BH4, a pteridine cofactor) and a non-heme iron for catalysis. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria